Cerebellar Ataxia and Neurosensory Deafness is characterized by ataxia and hearing loss. Only four cases from a single family (three brothers and one sister) have been reported with this disease worldwide. It appears to follow an autosomal recessive inheritance pattern.
Farag et al. (1993) screened 400 institutionalized intellectually disabled patients in Kuwait during a four years period from January 1986 to January 1990; one of the patients was found to be suffering from Cerebellar Ataxia and Neurosensory Deafness.