WHO-ICD-10 version:2010
Congenital malformations, deformations and chromosomal abnormalities
Other congenital malformations
Mode of Inheritance
Isolated cases
Gene Map Locus
Not Mapped
Hypoglossia with situs inversus is a very rare congenital malformation involving a partial to total absence of the tongue along with situs inverses which is a medical term for organs which are located on the wrong side of the body such as: heart on the right side of the body and liver on the left side of the body. The prevalence of this condition is unknown.
The exact genetic cause of hypoglossia with situs inversus is still unknown.