Lipoid Proteinosis of Urbach and Wiethe is a condition characterized by deposition of masses of hyaline material in the skin and mucous membranes, especially those of the mouth. One of the characteristic symptoms of the condition is hoarseness of voice, which can be seen in most affected patients right after birth, when the infant begins to cry. Skin lesions become apparent later in life. These lesions develop in two distinct stages: the first stage consisting of bulla and hemorrhagic crusts, followed by waxy, thickened skin along with verrucous lesions on the extensor surfaces. Hyperkeratosis is seen on the elbows, knees, and axilla. On the face as well as the extremities, pox-like or acneiform scars may appear. One of the most typical features of the condition is the presence of beaded papules on the eyelids. In some cases, patients may also show epilepsy and neuro-psychiatric abnormalities.