Left Ventricular Noncompaction 10

Alternative Names

  • LVNC10
  • Cardiomyopathy, Dilated
  • CMD1MM
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WHO-ICD-10 version:2010

Diseases of the circulatory system

Other forms of heart disease

OMIM Number

615396

Mode of Inheritance

Autosomal dominant

Gene Map Locus

11p11.2

Description

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events. [From Orphanet]

Epidemiology in the Arab World

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Subject IDCountrySexFamily HistoryParental ConsanguinityHPO TermsVariantZygosityMode of InheritanceReferenceRemarks
615396.1United Arab EmiratesUnknown Dilated cardiomyopathyNM_000256.3:c.776delinsTTHeterozygousAutosomal, DominantAl-Shamsi et al. 2016
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