Congenital pyloric atresia (CPA) is a very rare anomaly of the fetal gastrointestinal tract, causing gastric outlet obstruction already in utero and, later, in the neonatal period. Although CPA can occur in isolation, not uncommonly it is seen in association with either gastrointestinal atresias or epidermolysis bullosa (EB) and/or aplasia cutis congenital (ACC).
