Duodenal Atresia

Alternative Names

  • Duodenal Stenosis
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WHO-ICD-10 version:2010

Congenital malformations, deformations and chromosomal abnormalities

OMIM Number

223400

Mode of Inheritance

Autosomal Recessive

Description

Duodenal Atresia is a congenital condition characterised by underdevelopment of duodenum. It is the most common type of congenital small bowel obstruction with an incidence of approximately 1 in 10,000 live births. The clinical presentation depends on the degree of atresia that is present.  A classic sign is bilious vomiting without abdominal distention. Weight loss, dehydration and hypochloremic metabolic acidosis are common.

In most cases, the etiology of duodenal atresia is unknown. It is mostly sporadic but autosomal recessive pattern has been noted in some families.

Epidemiology in the Arab World

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Other Reports

Iraq

Nasir et al. (2000) reviewed 36 cases of neonatal intestinal obstruction over a period of 10 years in Basra General Hospital, Iraq. 13.9% cases were caused by duodenal atresia.

Lebanon

Mishalany et al. reported three cases of duodenal atresia in 1970 and 1971. All three patients were from consanguinous families. Der Kaloustian et al. (1974) reported yet another affected child.

United Arab Emirates

Nawaz et al. (1999) observed 10 patients with duodenal obstruction in a retrospective study conducted to evaluate patients with neonatal intestinal atresia.

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